Repeated treatments with rituximab in a patient with amyloid-like IgM deposition neuropathy
نویسندگان
چکیده
Amyloid-like immunoglobulin M (IgM) deposition neuropathy associated with Waldenström macroglobulinemia is a rare phenotype of IgM-related neuropathy. The prominent clinical features are painful sensory-dominant neuropathy followed by distal motor weakness and atrophy over a long clinical course that are refractory to immunosuppressive treatment in many patients. Herein, we report a case of amyloid-like IgM deposition neuropathy that was successfully treated with rituximab (RTX).
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